Intra-abdominal metastasis after pelvic primary Synovial Sarcoma resection: case report

  • Amal Hajri Department of general surgery, IBN ROCHD University hospital of Casablanca, Casablanca, Morocco
  • Khalid Jamaleddine Department of general surgery, IBN ROCHD University hospital of Casablanca, Casablanca, Morocco
  • Anas El Wassi Department of general surgery, IBN ROCHD University hospital of Casablanca, Casablanca, Morocco
  • Driss Erguibi Department of general surgery, IBN ROCHD University hospital of Casablanca, Casablanca, Morocco
  • Rachid Boufettal Department of general surgery, IBN ROCHD University hospital of Casablanca, Casablanca, Morocco
  • Saad Jai Rifki Department of general surgery, IBN ROCHD University hospital of Casablanca, Casablanca, Morocco
  • Farid Chehab Department of general surgery, IBN ROCHD University hospital of Casablanca, Casablanca, Morocco
Keywords: Synovial sarcoma; soft tissue sarcoma, metastatic sarcoma

Abstract

Introduction: Synovial sarcoma is a malignant soft tissue sarcoma. It occurs predominantly in young adults. 90% of synovial sarcomas occur in the extremities, they have been reported in other sites, including abdomen and pelvis. Up to 40% of all patients with soft tissue sarcomas develop distant metastasis, despite adequate local disease control.

Aim of the article: To provide an update on one of the rarest and most aggressive tumors, to affirm the importance of early management and especially surveillance, and to encourage the codification and the management of these tumors.

Presentation of cases: Here, we discuss a case of a 78-year-old female patient, operated 10 years earlier for a pelvic Synovial sarcoma, who presented with intra-abdominal mass to our hospital that eventually turned out to be a metastatic intra-abdominal synovial sarcoma following biopsy.

Conclusion: It is important to be aware that primary intraabdominal tumors can occur and delayed metastasis is more typical of synovial sarcoma than of many other sarcomas and should be considered in determining the appropriate frequency and duration of follow-up imaging.

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Published
2024-05-21
How to Cite
Hajri, A., Jamaleddine, K., El Wassi, A., Erguibi, D., Boufettal, R., Jai Rifki, S., & Chehab, F. (2024). Intra-abdominal metastasis after pelvic primary Synovial Sarcoma resection: case report. European Scientific Journal, ESJ, 29, 539. Retrieved from https://eujournal.org/index.php/esj/article/view/18157
Section
ESI Preprints